Citation Information :
Maruduraj V, Gopalan M, Kumar AN, Navidh F, Bhooshan S, Priya M. A Rare Case of Recurrent Pseudomyxomatous Peritonei Presenting as Peritoneo-cutaneous Fistula: A Case Report. 2022; 5 (4):92-96.
Pseudomyxoma peritonei (PMP) is a rare disorder, characterized by diffuse intra-abdominal gelatinous contents, the so-called “jelly belly like content,” with mucinous implants on the peritoneal surface. We report a case of an 84-year-old female, with a history of abdominal diffuse swelling for 7 years and yellow jelly-like discharge below the umbilicus. Abdominal ultrasonography and CT scan of the abdomen showed the jelly-like collection in the entire abdomen and pelvis extending through the subcutaneous plane. Laparotomy showed cheese burst defect in linea alba and yellow jelly-like mucinous fluid. The histological study revealed mucinous cells. The patient had a good postoperative performance status. Pseudomyxomatous peritonei describes the peritoneal dissemination of mucus-producing tumors, most frequently from the appendix but also occurs in the small and large bowel, stomach, pancreas, lung, breast, gallbladder, fallopian tubes, and ovaries. Due to its aggressive behavior, often discovered incidentally at a relatively advanced stage during screening for other medical concerns. PMP demands consideration as a ‘borderline malignancy’ with a differential prognosis based on the site of origin.
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